PReS-FINAL-2300: Shrinking lung syndrome in an adolescent male with juvenile systemic lupus erythematosus
نویسندگان
چکیده
Introduction Pulmonary involvement occurs in up to 80% of Systemic Lupus Erythematosus (SLE) patients, with decreased diffusing capacity (DLCO) and interstitial lung disease being most common. Shrinking lung syndrome (SLS) is a rare complication, which consists in small lung volumes, elevation of the diaphragm and restrictive physiology without parenchymal or pleural involvement. Its pathogenesis remains controversial, and anomalies such as diaphragm dysfunction, phrenic neuropathy, respiratory muscles myopathy and pleural inflammation have been hypothesized.
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